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ORPHA:563Disease
Also called Postpartum cardiomyopathy
What it is
Peripartum cardiomyopathy (PPCM) is an idiopathic, potentially fatal form of dilated cardiomyopathy that develops during the final month of pregnancy or within five months after delivery.
Key facts
- Prevalence
- 6-9 / 10 000 (at birth, Singapore)
- Age of onset
- Adult
- Inheritance
- Unknown
- Classified as
- Disease
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Signs and symptoms
Common30–79%
16- Abnormal T-wave
- Congestive heart failure
- Dilated cardiomyopathy
- Dyspnea
- Elevated jugular venous pressure
- Exertional dyspnea
- Fatigue
- Hypertension
- Left ventricular hypertrophy
- Left ventricular systolic dysfunction
- Orthopnea
- Palpitations
- Pedal edema
- Reduced left ventricular ejection fraction
- Sinus tachycardia
- Tachycardia
Sometimes5–29%
18- Abnormal atrioventricular valve morphology
- Abnormal cardiac atrium morphology
- Chest pain
- Crackles
- Heart murmur
- Increased serum interferon-gamma level
- Left atrial enlargement
- Mitral regurgitation
and 10 more in this range
Rare1–4%
11- Abdominal pain
- Abnormality of thyroid physiology
- Anemia
- Asthma
- Autoimmunity
- Cardiogenic shock
- Diabetes mellitus
- Left bundle branch block
and 3 more in this range
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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