MALT lymphoma

Caring for someone with this diagnosis? Eleplan keeps diagnoses, medications, documents and every specialist in one plan.

Start free with Eleplan

MALT lymphoma

ORPHA:52417Disease

Also called Extranodal marginal zone B-cell lymphoma · MALToma · Mucosa-associated lymphatic tissue lymphoma · Mucosa-associated lymphoid tissue lymphoma

What it is

MALT (mucosa-associated lymphoid tissue) lymphoma is a rare form of malignant non-Hodgkin lymphoma that affects B cells and grows at the expense of lymphoid tissue associated with mucous membranes, but also occurs, more rarely, in lymph nodes.

Key facts

Prevalence
1-9 / 100 000 (Europe)
Age of onset
Adult
Inheritance
Multigenic/multifactorial, Not applicable
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

Genes

BCL10Part of a fusion gene
BIRC3Part of a fusion gene
FOXP1Part of a fusion gene
IGHPart of a fusion gene
MALT1Part of a fusion gene

ICD-10 codes

C88.4ICD-10 names this disease exactly

Cross-references

GARD 6485MEDDRA 10060707MONDO 0007650OMIM 137245UMLS C1850900

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

Powered by Eleplan

A rare diagnosis is just the start. Eleplan keeps the whole care plan in one place.

Diagnoses, medications, documents, appointments, and the whole care team — organized and always in sync, so you are not retelling the same story to every new specialist. With Ellie, your AI care assistant, on top of it. Free to start.