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Start free with EleplanImmunoglobulin A vasculitis
ORPHA:761Disease
Also called Anaphylactoid purpura · Henoch-Schönlein purpura · IgA vasculitis · Purpura rheumatica · Rheumatoid purpura
What it is
A rare, small-vessel vasculitis characterized by skin purpura, arthritis, abdominal and/or renal involvement, IgA tissue deposits (arterioles, capillaries, and venules) and circulating IgA immune complexes.
Key facts
- Prevalence
- 6-9 / 10 000 (annual incidence, Korea, Republic of)
- Age of onset
- Childhood
- Inheritance
- Not applicable
- Classified as
- Disease
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Signs and symptoms
Very common80–99%
10Common30–79%
10Sometimes5–29%
14- Angioedema
- Edema
- Episcleritis
- Gastrointestinal hemorrhage
- Glomerulopathy
- Hemiplegia/hemiparesis
- Macule
- Muscle weakness
and 6 more in this range
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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