Classic Hodgkin lymphoma

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Classic Hodgkin lymphoma

ORPHA:391Disease

Also called Classic Hodgkin disease

What it is

Classical Hodgkin lymphoma (CHL) is a B-cell lymphoma characterized histologically by the presence of large mononuclear Hodgkin cells and multinucleated Reed-Sternberg (HRS) cells.

Key facts

Prevalence
1-5 / 10 000 (Europe)
Age of onset
All ages
Inheritance
Unknown
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

Genes reported in subtypes

KLHDC8B

Orphanet records this gene on 1 more specific entry under this disorder, not on this entry itself:

A well-studied disease is usually split into subtypes, and the gene is curated on whichever one the evidence belongs to. Open a subtype to see which gene goes with it.

ICD-10 codes

C81.0ICD-10 uses a narrower term — shared with 1 other rare disease
C81.1ICD-10 uses a narrower term — shared with 1 other rare disease
C81.2ICD-10 uses a narrower term — shared with 1 other rare disease
C81.3ICD-10 uses a narrower term — shared with 1 other rare disease
C81.4ICD-10 uses a narrower term — shared with 1 other rare disease
C81.7ICD-10 uses a narrower term — shared with 1 other rare disease
C81.9ICD-10 uses a narrower term

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

MONDO 0009348OMIM 236000OMIM 300221OMIM 400021UMLS C1333064

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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