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Start free with EleplanIsolated atrial standstill
ORPHA:1344Disease
Also called Isolated atrial cardiomyopathy with heart block
What it is
A rare cardiac rhythm disease characterized by a transient or permanent absence of electrical and mechanical atrial activity. Electrocardiographic findings include bradycardia, ectopic supraventricular rhythms, lack of atrial excitability and absent P waves.
Key facts
- Age of onset
- Adult
- Inheritance
- Autosomal dominant, Not applicable
- Classified as
- Disease
Signs and symptoms
Very common80–99%
5Common30–79%
11Sometimes5–29%
16- Aphasia
- Bradycardia
- Cardiomyopathy
- Congestive heart failure
- Dysarthria
- Flexion contracture
- Headache
- Hemiplegia
and 8 more in this range
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
Genes
ICD-10 codes
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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