Acute promyelocytic leukemia

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Acute promyelocytic leukemia

ORPHA:520Disease

Also called AML M3 · AML with t(15;17)(q22;q12);(PML/RARalpha) and variants · APML · Acute myeloblastic leukemia 3 · Acute myeloid leukemia with t(15;17)(q22;q12);(PML/RARalpha) and variants

What it is

An aggressive form of acute myeloid leukemia (AML), characterized by arrest of leukocyte differentiation at the promyelocyte stage, due to a specific chromosomal translocation t(15;17) in myeloid cells, and manifests with easy bruising, hemorrhagic diathesis and fatigue.

Key facts

Prevalence
1-9 / 1 000 000 (annual incidence, Europe)
Age of onset
Adolescent, Adult, Childhood, Elderly
Inheritance
Not applicable
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

Genes

BCORPart of a fusion gene
FIP1L1Part of a fusion gene
IRF2BP2Part of a fusion gene
NABP1Part of a fusion gene
NPM1Part of a fusion gene
NUMA1Part of a fusion gene
PMLPart of a fusion gene
PRKAR1APart of a fusion gene
RARAPart of a fusion gene
STAT3Part of a fusion gene
STAT5BPart of a fusion gene
TBL1XR1Part of a fusion gene
ZBTB16Part of a fusion gene

ICD-10 codes

C92.4ICD-10 names this disease exactly

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

GARD 538MEDDRA 10001019MESH D015473MONDO 0012883OMIM 612376UMLS C0023487

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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