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Start free with EleplanRetinal cavernous hemangioma
ORPHA:71213Disease
Also called Cavernous hemangioma of the retina · RCH
What it is
Retinal cavernous hemangioma is a rare, benign, usually unilateral retinal vascular hamartoma that in most cases is asymptomatic but in some patients may present with blurred vision or floaters and that is characterized by the presence of grape-like vacuoles.
Key facts
- Age of onset
- All ages
- Inheritance
- Autosomal dominant
- Classified as
- Disease
Signs and symptoms
Sometimes5–29%
17- Amblyopia
- Anisometropia
- Blindness
- Blurred vision
- Central fundal arteriolar microaneurysms
- Epiretinal membrane
- Glaucoma
- Hyphema
and 9 more in this range
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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