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Start free with EleplanChronic inflammatory demyelinating polyneuropathy
ORPHA:2932Disease
Also called CIDP · Chronic inflammatory demyelinating polyradiculoneuropathy
What it is
A rare chronic monophasic progressive or relapsing symmetric sensorimotor disorder characterized by progressive muscular weakness with impaired sensation, absent or diminished tendon reflexes, electrodiagnostic features suggestive of demyelination and occasional elevated cerebrospinal fluid (CSF) protein level.
Key facts
- Prevalence
- 1-9 / 100 000 (Italy)
- Age of onset
- Adolescent, Adult, Childhood, Elderly
- Inheritance
- Not applicable
- Classified as
- Disease
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Signs and symptoms
Very common80–99%
12- Abnormal nerve conduction velocityDiagnostic criterion
- Areflexia
- Decreased nerve conduction velocityDiagnostic criterion
- Fatiguable weakness of proximal limb musclesDiagnostic criterion
- Motor conduction block
- Paresthesia
- Peripheral demyelination
- Peripheral neuropathy
- Segmental peripheral demyelination/remyelination
- Sensory ataxia
- Somatic sensory dysfunction
- Unsteady gait
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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