Rare diseases · Sign or symptom
Unsteady gait
Unsteady walk
HP:0002317
Rare diseases that can present with this75
Very common80–99%
8- Adenylosuccinate synthetase-like 1-related distal myopathy
- Ataxia-pancytopenia syndrome
- Autosomal spastic paraplegia type 30
- Chronic inflammatory demyelinating polyneuropathy
- Progressive supranuclear palsy
- Progressive supranuclear palsy-pure akinesia with gait freezing syndrome
- Spinocerebellar ataxia type 42
- Spinocerebellar ataxia type 6
Common30–79%
49- 7q11.23microduplication syndrome
- Acute inflammatory demyelinating polyradiculoneuropathy
- Adult-onset cervical dystonia, DYT23 type
- Alpha-dystroglycan-related limb-girdle muscular dystrophy R16
- Atypical progressive supranuclear palsy syndrome
- Autosomal dominant optic atrophy and cataract
- Autosomal recessive cerebellar ataxia due to CWF19L1 deficiency
- Autosomal recessive cerebellar ataxia due to STUB1 deficiency
- Autosomal recessive cerebellar ataxia-movement disorder syndrome
- Autosomal recessive cerebellar ataxia-psychomotor delay syndrome
- Autosomal recessive Charcot-Marie-Tooth disease with hoarseness
- Autosomal recessive spastic ataxia of Charlevoix-Saguenay
- Autosomal recessive spastic paraplegia type 28
- Autosomal recessive spastic paraplegia type 56
- Charcot-Marie-Tooth disease type 1F
- Charcot-Marie-Tooth disease type 4A
- Charcot-Marie-Tooth disease type 4D
- Childhood-onset spasticity with hyperglycinemia
- Cockayne syndrome type 3
- Distal hereditary motor neuropathy type 5
- Dystonia 16
- Dystonia-aphonia syndrome
- Giant axonal neuropathy
- GM1 gangliosidosis
- Houge-Janssens syndrome type 1
- Hyperprolinemia type 2
- Ichthyosis-alopecia-eclabion-ectropion-intellectual disability syndrome
- Infantile-onset generalized dyskinesia with orofacial involvement
- Intellectual disability-balding-patella luxation-acromicria syndrome
- Leukoencephalopathy with brain stem and spinal cord involvement-high lactate syndrome
- Mal de débarquement
- Megalencephalic leukoencephalopathy with subcortical cysts
- Myxopapillary ependymoma
- Non-progressive cerebellar ataxia with intellectual disability
- Northern epilepsy
- PLA2G6-related neurodegeneration, infantile-onset
- Pyridoxamine-5-phosphate deficiency-developmental and epileptic encephalopathy
- Roussy-Lévy syndrome
- Spastic paraplegia-severe developmental delay-epilepsy syndrome
- Spinocerebellar ataxia type 10
- Spinocerebellar ataxia type 40
- Spinocerebellar ataxia type 43
- Spinocerebellar ataxia type 8
- Sydenham chorea
- Vocal cord and pharyngeal distal myopathy
- X-linked intellectual disability, Hedera type
- X-linked intellectual disability, Snyder type
- X-linked non progressive cerebellar ataxia
- X-linked progressive cerebellar ataxia
Sometimes5–29%
15- Autosomal spastic paraplegia type 58
- Bilateral striopallidodentate calcinosis
- Distal deletion 10q syndrome
- Fatal infantile lactic acidosis with methylmalonic aciduria
- Full NF2-related schwannomatosis
- Intellectual disability-epilepsy-extrapyramidal syndrome
- Non-specific early-onset epileptic encephalopathy
- Paraneoplastic cerebellar degeneration
and 7 more in this range
The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.
Part of the broader category
Also called: Gait instability
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Start free with EleplanThis page uses the Human Phenotype Ontology (2026-06-23) — Human Phenotype Ontology Consortium, hpo.jax.org. Disease associations from Orphanet (INSERM), CC BY 4.0. Content is educational and is not medical advice.