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Start free with EleplanSchilder disease
ORPHA:59298Disease
Also called Myelinoclastic diffuse sclerosis
What it is
Schilder's disease is a progressive demyelinating disorder of the central nervous system.
Key facts
- Age of onset
- Childhood
- Classified as
- Disease
Signs and symptoms
Common30–79%
6Sometimes5–29%
13- Ankle clonus
- Ataxia
- CSF pleocytosis
- Diplopia
- Encephalopathy
- Esotropia
- Increased intracranial pressure
- Muscle weakness
and 5 more in this range
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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