His bundle tachycardia

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His bundle tachycardia

ORPHA:3283Disease

Also called JET · Junctional ectopic tachycardia

What it is

His bundle tachycardia is a very rare congenital genetic tachyarrhythmia characterized by incessant tachycardia and high morbidity and mortality.

Key facts

Age of onset
Infancy, Neonatal
Inheritance
Unknown
Classified as
Disease

Signs and symptoms

Common30–79%

1

Sometimes5–29%

1

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

ICD-10 codes

I47.1filed under a broader ICD-10 category — shared with 1 other rare disease

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Cross-references

GARD 2706MEDDRA 10074640MESH D013613MONDO 0017989UMLS C0039235

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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