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Non-billableEncephalocele
Q01 is the ICD-10-CM code for Encephalocele. It is a non-billable category code — use a more specific child code such as Q01.0 for billing.
- Status
- Header (non-billable)
- Chapter
- Q00-Q99
- Subcodes
- 5
- Edition
- FY2026
Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities
What this means — in plain language
MedlinePlus · NIHNeural tube defects are birth defects of the brain, spine, or spinal cord. They happen in the first month of pregnancy, often before a woman even knows that she is pregnant. The two most common neural tube defects are spina bifida and anencephaly. In spina bifida, the fetal spinal column doesn't close completely. There is usually nerve damage that causes at least some paralysis of the legs. In anencephaly, most of…
Read more about Neural Tube Defects at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Includes
- •Arnold-Chiari syndrome, type III
- •encephalocystocele
- •encephalomyelocele
- •hydroencephalocele
- •hydromeningocele, cranial
- •meningocele, cerebral
- •meningoencephalocele
Excludes1 — not coded here
- •Meckel-Gruber syndrome (Q61.9)
Conditions mapped to this code
MedlinePlus · NIHPlain-language health-topic references grounded in MedlinePlus (NIH/NLM).
16 rare diseases filed under this code
Orphanet · INSERMICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. This code is shared — showing 12 of 16.
Orphadata Science: Free access data from Orphanet. © INSERM 1999. 4 of these are exact ICD-10 matches; the rest are broader-bucket mappings.
Frequently asked questions
- What is ICD-10 code Q01?
- Q01 is the ICD-10-CM code for "Encephalocele". It falls under Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities.
- Is Q01 a billable code?
- No — Q01 is a non-billable header code. Use a more specific child code (such as Q01.0) for billing.
- What is excluded from Q01?
- Excludes1 (not coded here): Meckel-Gruber syndrome (Q61.9).
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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