Rare diseases · Sign or symptom

Unilateral deafness

Deafness in one ear

HP:0009900

What it means

A unilateral absence of sensory perception of sound.

Deafness affecting only one ear.

Rare diseases that can present with this2

The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.

Part of the broader category

Also called: Deafness, unilateral

Unilateral deafness

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This page uses the Human Phenotype Ontology (2026-06-23) — Human Phenotype Ontology Consortium, hpo.jax.org. Disease associations from Orphanet (INSERM), CC BY 4.0. Content is educational and is not medical advice.