Rare diseases · Sign or symptom
Posterior helix pit
Indentation in back of outer ear
HP:0008523
What it means
Permanent indentation on the posteromedial aspect of the helix that may be sharply or indistinctly delineated.
They are usually linear to a narrow oval in shape and may be single or multiple.
Rare diseases that can present with this1
The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.
Part of the broader category
Also called: Ear, posterior helical groove · Ear, posterior helical notch · Helix, posterior pit · Pits in posterior aspect of ear helices
Tracking symptoms like this for someone? Eleplan keeps symptoms, diagnoses, medications and every specialist in one plan.
Start free with EleplanThis page uses the Human Phenotype Ontology (2026-06-23) — Human Phenotype Ontology Consortium, hpo.jax.org. Disease associations from Orphanet (INSERM), CC BY 4.0. Content is educational and is not medical advice.