Ichthyosis linearis circumflexa

What it means

A type of ichthyosis characterized by migratory, annular and polycyclic erythematous patches with double-edged scales at the periphery of the lesions.

The erythematous patch (flat area of redness 1 cm or more in width) that is ring-shaped (annular) or serpiginous (with multiple ring-shaped lesions (polycyclic). The lesions are bordered by two distinct rings of scale at their outer edges (double-edged). The distribution of the lesions changes with time (migratory). Ichthyosis linearis circumflexa (ILC) may rarely be observed as an isolated lesion, but is a characteristic manifestation of Netherton syndrome. Lesions are often described as serpiginous scaling or double-edged scaling.

Rare diseases that can present with this1

The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.

Part of the broader category

Also called: Double-edged scaling · Serpiginous scaling