Rare diseases · Sign or symptom
Atrioventricular block
Interruption of electrical communication between upper and lower chambers of heart
HP:0001678
What it means
Delayed or lack of conduction of atrial depolarizations through the atrioventricular node to the ventricles.
Rare diseases that can present with this23
Common30–79%
7Sometimes5–29%
13- Atrial septal defect, ostium primum type
- Autosomal dominant Emery-Dreifuss muscular dystrophy
- Complete atrioventricular septal defect
- Congenital short QT syndrome
- Emery-Dreifuss muscular dystrophy
- Histiocytoid cardiomyopathy
- Idiopathic giant cell myocarditis
- Lyme disease
and 5 more in this range
The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.
Part of the broader category
Also called: Atrioventricular nodal disease
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Start free with EleplanThis page uses the Human Phenotype Ontology (2026-06-23) — Human Phenotype Ontology Consortium, hpo.jax.org. Disease associations from Orphanet (INSERM), CC BY 4.0. Content is educational and is not medical advice.