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Start free with EleplanRenal hypoplasia, unilateral
ORPHA:97361Clinical subtype
What it is
A form of renal hypoplasia characterized by unilateral abnormally small kidneys with reduced number of nephrons. Patients are usually asymptomatic however some patients may present with hypertension and urinary tract infections. Risk of renal failure in childhood is minimal.
Key facts
- Age of onset
- All ages
- Inheritance
- Not applicable
- Classified as
- Clinical subtype
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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