Pulmonary interstitial glycogenosis

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Pulmonary interstitial glycogenosis

ORPHA:217557Disease

Also called Infantile cellular interstitial pneumonitis · PIG

What it is

Pulmonary interstitial glycogenosis (PIG) is a rare non-lethal pediatric form of interstitial lung disease (ILD).

Key facts

Age of onset
Infancy, Neonatal
Inheritance
Not applicable
Classified as
Disease

ICD-10 codes

P22.8filed under a broader ICD-10 category

Cross-references

MONDO 0016321UMLS C3161106

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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