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Start free with EleplanNon-malignant and non-cirrhotic portal vein thrombosis
ORPHA:854Clinical syndrome
Also called Non-cirrhotic and non-tumoral portal vein thrombosis · Non-malignant non-cirrhotic PVT
What it is
Portal vein thrombosis (PVT) is associated with acute (recent) or chronic (long-standing) thrombosis of the portal system.
Key facts
- Prevalence
- 1-9 / 100 000 (Sweden)
- Age of onset
- All ages
- Inheritance
- Not applicable
- Classified as
- Clinical syndrome
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
ICD-10 codes
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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