Neuralgic amyotrophy

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Neuralgic amyotrophy

ORPHA:2901Disease

Also called Acute brachial plexus neuritis · Brachial plexus neuritis · Immune brachial plexus neuropathy · Mononeuritis multiplex with brachial predilection · Neuralgic shoulder amyotrophy

What it is

A rare disorder of the peripheral nervous system characterized by the sudden onset of extreme pain in the upper extremity followed by rapid multifocal motor weakness and atrophy and a slow recovery in months to years. NA includes both an idiopathic (INA, also known as Parsonage-Turner syndrome) and hereditary (HNA) form.

Key facts

Prevalence
1-5 / 10 000 (Europe)
Age of onset
Adult
Inheritance
Autosomal dominant, Not applicable
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

Gene

SEPTIN9Major susceptibility factor

ICD-10 codes

G54.5filed under a broader ICD-10 category

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

GARD 4228MEDDRA 10029229MESH D020968MONDO 0017362OMIM 162100UMLS C1510479

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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