Isolated arhinencephaly

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Isolated arhinencephaly

ORPHA:268936Morphological anomaly

What it is

Isolated arhinencephaly is a rare non-syndromic central nervous system malformation defined by the agenesis of the olfactory bulbs and tracts and characterized by complete congenital anosmia.

Key facts

Age of onset
Infancy, Neonatal
Classified as
Morphological anomaly

ICD-10 codes

Q04.1ICD-10 names this disease exactly

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

MONDO 0968959MONDO 968959UMLS C4749732

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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