IgG4-related mesenteritis

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IgG4-related mesenteritis

ORPHA:238593Clinical subtype

Also called Isolated mesenteric lipodystrophy · Lipomatous mesenteritis · Liposclerotic mesenteritis · Mesenteric lipogranuloma · Mesenteric panniculitis · Sclerosing mesenteritis

What it is

Sclerosing mesenteritis (SM) is a rare pathological disease causing inflammation of the adipose tissue of the small bowel mesentery and is commonly associated with abdominal pain, diarrhea, nausea, weight loss, bloating and loss of appetite. The two subforms include mesenteric panniculitis (where inflammation and fatty necrosis are dominant features) and retractile mesenteritis (where fibrosis and retraction dominate).

Key facts

Age of onset
Adult
Inheritance
Not applicable
Classified as
Clinical subtype

ICD-10 codes

K65.8filed under a broader ICD-10 category

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

GARD 8169MEDDRA 10063031MONDO 0016544UMLS C0267770

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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