Generalized lymphatic anomaly

Caring for someone with this diagnosis? Eleplan keeps diagnoses, medications, documents and every specialist in one plan.

Start free with Eleplan

Generalized lymphatic anomaly

ORPHA:141209Malformation syndrome

Also called Diffuse lymphangioma · Diffuse lymphangiomatosis · Disseminated lymphangioma · Disseminated lymphangiomatosis · Disseminated lymphatic malformation · GLA · Diffuse lymphatic malformation

What it is

A rare developmental defect during embryogenesis characterized by multifocal dilated lymphatic vessels involving multiple organs and tissues. Patients mostly present in infancy and childhood. Clinical course and prognosis depend on the affected sites and extent of the condition, deterioration of lung function being a major cause of morbidity and mortality.

Key facts

Age of onset
Infancy, Neonatal
Inheritance
Not applicable
Classified as
Malformation syndrome

ICD-10 codes

I89.8filed under a broader ICD-10 category — shared with 1 other rare disease

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

GARD 19961MONDO 0015408UMLS C3839921

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

Powered by Eleplan

A rare diagnosis is just the start. Eleplan keeps the whole care plan in one place.

Diagnoses, medications, documents, appointments, and the whole care team — organized and always in sync, so you are not retelling the same story to every new specialist. With Ellie, your AI care assistant, on top of it. Free to start.