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Start free with EleplanClassic eosinophilic pustular folliculitis
ORPHA:617408Disease
Also called Classic EPF · Ofuji disease
What it is
A rare skin disease characterized by non-infectious eosinophilic infiltration of the hair follicles. Patients present with chronically recurrent crops of itchy follicular papulopustules with peripheral extension and central clearing. Small papules tend to enlarge and coalesce into large plaques. The lesions favor the face and trunk, although the extremities can also be involved. Laboratory analysis may show peripheral leukocytosis and eosinophilia, while, clinically, systemic involvement is not evident.
Key facts
- Age of onset
- Adolescent, Adult
- Inheritance
- Not applicable
- Classified as
- Disease
ICD-10 codes
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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