Celiac artery compression syndrome

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Celiac artery compression syndrome

ORPHA:293208Disease

Also called Dunbar syndrome · MALS · Median arcuate ligament syndrome

What it is

A rare disease caused by compression of the celiac axis by an abnormally shaped arcuate ligament (the part of the diaphragm in which both pillars join in the midline around the aorta). Patients have recurrent abdominal pain, anorexia and weight loss. The pain is epigastric, and diarrhea or constipation may be present as well. Onset of pain will usually, although not always, be after food intake, and may be associated with nausea and emesis. Other symptoms may include lassitude, exercise intolerance and vomiting. Occasionally, a patient may show an abdominal murmur upon auscultation.

Key facts

Age of onset
Adolescent, Adult, Childhood, Elderly
Inheritance
Not applicable
Classified as
Disease

ICD-10 codes

I77.4ICD-10 names this disease exactly

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

GARD 12308MEDDRA 10009838MONDO 0017388MONDO 17388UMLS C1861783

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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