Venous thoracic outlet syndrome

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Venous thoracic outlet syndrome

ORPHA:357131Clinical subtype

Also called Venous scalenus anticus syndrome · Venous thoracic outlet compression syndrome · Effort subclavian vein thrombosis · Paget-Schrotter disease · VTOS · Venous TOS · Venous cervical rib syndrome · Venous costoclavicular syndrome · Venous hyperabduction syndrome

What it is

Venous thoracic outlet syndrome (VTOS) is a form of thoracic outlet syndrome (TOS) that manifests as unilateral (rarely bilateral) arm pain and cyanosis.

Key facts

Inheritance
Not applicable
Classified as
Clinical subtype

ICD-10 codes

G54.0filed under a broader ICD-10 category — shared with 4 other rare diseases

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

MONDO 0018165UMLS C1956396

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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