Small bowel atresia

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Small bowel atresia

ORPHA:1201Morphological anomaly

Also called Atresia of small bowel · Atresia of small intestine · Jejunal atresia · Jejunoileal atresia · SBA · Small intestinal atresia

What it is

A rare, congenital defect of the small intestine characterized by disruption in the normal small intestine continuity, resulting in intestinal obstruction. The malformation may be classified in four different types of small bowel atresia (SBA) based on the anatomical obstruction.

Key facts

Prevalence
1-9 / 100 000 (at birth, Europe)
Age of onset
Antenatal
Inheritance
Autosomal recessive, Not applicable, Unknown
Classified as
Morphological anomaly

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

ICD-10 codes

Q41.0ICD-10 uses a narrower term — shared with 1 other rare disease
Q41.1ICD-10 uses a narrower term
Q41.2ICD-10 uses a narrower term
Q41.8ICD-10 uses a narrower term
Q41.9ICD-10 uses a narrower term — shared with 1 other rare disease

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Cross-references

GARD 140MEDDRA 10010626MESH C538260MONDO 0009476OMIM 243600UMLS C0266172

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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