Total anomalous pulmonary venous return

What it means

Total anomalous pulmonary venous return refers to a congenital malformation in which all four pulmonary veins do not connect normally to the left atrium, but instead drain abnormally to the right atrium.

Pulmonary veins drain through abnormal connections to the right atrium.

Rare diseases that can present with this3

The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.

Part of the broader category

Also called: TAPVC · TAPVD · TAPVR · Total anomalous pulmonary venous connection · Total anomalous pulmonary venous drainage