Pulmonary sequestration

What it means

The presence of a piece lung tissue which is not attached to the pulmonary blood supply and does not communicate with the other lung tissue (not connected to the standard bronchial airways and not performing a function in respiration).

Typically, the sequestered lung tissue receives all or most of its blood supply from an anomalous systemic artery, with the origin of this artery being variable.

Rare diseases that can present with this4

The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.

Part of the broader category

Also called: Bronchopulmonary sequestration · Cystic lung lesion