Histidinuria

What it means

An increased concentration of histidine in the urine.

Normal urinary histidine total (free and combined form) excretion is around 190 mg per 24 hours.

Rare diseases that can present with this2

The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.

Part of the broader category

Also called: Elevated histidine in urine