Rare diseases · Sign or symptom
Dextrocardia
Heart tip and four chambers point towards right side of body
HP:0001651
What it means
The heart is located in the right hand sided hemithorax. That is, there is a left-right reversal (or "mirror reflection") of the anatomical location of the heart in which the heart is locate on the right side instead of the left.
Rare diseases that can present with this23
Very common80–99%
2Sometimes5–29%
14- 8p inverted duplication/deletion syndrome
- Cardiac diverticulum
- Congenitally corrected transposition of the great arteries
- Congenital total pulmonary venous return anomaly
- Czeizel-Losonci syndrome
- Distal duplication 5q syndrome
- Johanson-Blizzard syndrome
- Joubert syndrome with ocular anomaly
and 6 more in this range
The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.
Part of the broader category
Also called: Thoracic situs inversus
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Start free with EleplanThis page uses the Human Phenotype Ontology (2026-06-23) — Human Phenotype Ontology Consortium, hpo.jax.org. Disease associations from Orphanet (INSERM), CC BY 4.0. Content is educational and is not medical advice.