Abnormal urine alpha-ketoglutarate concentration

What it means

A deviation from normal of the concentration of 2-oxoglutaric acid in the urine.

Note that alpha-ketoglutaric acid is also known as 2-ketoglutaric acid, alpha-ketoglutaric acid, 2-xxoglutaric acid, and oxoglutaric acid.

Rare diseases that can present with this1

The range is how often this sign appears among people diagnosed with each disease — it is not a probability of having any of them. Many of these signs also occur in common, non-rare conditions. A sign on this page is a conversation to have with a clinician, not a conclusion.

Part of the broader category

Also called: Abnormal urinary 2-oxoglutarate level · Abnormality of urine alpha ketoglutarate concentration