Salivary gland type cancer of the breast

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Salivary gland type cancer of the breast

ORPHA:213557Disease

Also called Salivary gland type carcinoma of the breast

What it is

Salivary gland type cancer of the breast describes a group of uncommon neoplasms, usually seen in the salivary glands but occurring in the breast, with a variable clinicopathologic spectrum and divided into those with myoepithelial differentiation and those without. This group includes mammary adenoid cystic carcinoma, adenoid cystic carcinoma, mucoepidermoid carcinoma, acinic cell carcinoma, polymorphous low-grade adenocarcinoma and oncocytic carcinoma.

Key facts

Prevalence
<1 / 1 000 000 (annual incidence, Europe)
Age of onset
Adult
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

ICD-10 codes

C50.0ICD-10 uses a narrower term — shared with 3 other rare diseases
C50.1ICD-10 uses a narrower term — shared with 2 other rare diseases
C50.2ICD-10 uses a narrower term — shared with 2 other rare diseases
C50.3ICD-10 uses a narrower term — shared with 2 other rare diseases
C50.4ICD-10 uses a narrower term — shared with 2 other rare diseases
C50.5ICD-10 uses a narrower term — shared with 2 other rare diseases
C50.6ICD-10 uses a narrower term — shared with 2 other rare diseases
C50.8ICD-10 uses a narrower term — shared with 2 other rare diseases

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Related health topics

Breast CancerMale Breast Cancer

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

MONDO 0100508UMLS C4274421

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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