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Start free with EleplanPulmonary arterial hypertension associated with portal hypertension
ORPHA:275813Clinical group
Also called PAH associated with portal hypertension · POPH · Portopulmonary hypertension
What it is
Pulmonary arterial hypertension associated with portal hypertension (PAH-PH) is a form of pulmonary arterial hypertension (PAH), characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of portal hypertension.
Key facts
- Age of onset
- Adult
- Inheritance
- No data available
- Classified as
- Clinical group
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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