Pulmonary arterial hypertension associated

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Pulmonary arterial hypertension associated with portal hypertension

ORPHA:275813Clinical group

Also called PAH associated with portal hypertension · POPH · Portopulmonary hypertension

What it is

Pulmonary arterial hypertension associated with portal hypertension (PAH-PH) is a form of pulmonary arterial hypertension (PAH), characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of portal hypertension.

Key facts

Age of onset
Adult
Inheritance
No data available
Classified as
Clinical group

Cross-references

MEDDRA 10067281MONDO 17154UMLS C1868851

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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