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Start free with EleplanPulmonary arterial hypertension associated with another disease
ORPHA:275791Category
Also called PAH associated with another disease · Secondary PAH
What it is
Pulmonary arterial hypertension associated with another disease is a group of conditions that lead to PAH; connective tissue diseases (lupus erythematosus, systemic sclerosis and mixed connective tissues disease), congenital heart disease (Eisenmenger syndrome), HIV infection, portal hypertension, schistosomiasis and chronic hemolytic anemia,which is characterized by elevated pulmonary arterial resistance leading to right heart failure that is progressive and potentially fatal.
Key facts
- Age of onset
- All ages
- Inheritance
- Not applicable
- Classified as
- Category
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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