Primary cutaneous lymphoma

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Primary cutaneous lymphoma

ORPHA:542Category

What it is

A group of rare primary organ-specific lymphoma characterized by heterogeneous T-cell and B-cell non-Hodgkin lymphomas present in the skin. Clinical and pathological features, evolutive profile, prognosis, molecular etiology and response to therapy are highly variable between the entities belong to this group.

Key facts

Prevalence
1-9 / 100 000 (Europe)
Classified as
Category

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Cross-references

MEDDRA 10051708MONDO 0018898MONDO 18898UMLS C1302772

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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