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Start free with EleplanPartial pancreatic agenesis
ORPHA:2805Morphological anomaly
Also called Congenital pancreatic agenesis · Partial agenesis of the pancreas
What it is
Partial agenesis of the pancreas is characterized by the congenital absence of a critical mass of pancreatic tissue.
Key facts
- Prevalence
- <1 / 1 000 000
- Age of onset
- Infancy, Neonatal
- Inheritance
- Autosomal recessive
- Classified as
- Morphological anomaly
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Genes
ICD-10 codes
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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