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Start free with EleplanMicrocystic lymphatic malformation
ORPHA:79490Clinical subtype
Also called Capillary lymphangioma · Capillary lymphatic malformation · Cutaneous lymphangioma circumscriptum · Microcystic infiltrating lymphatic malformation · Microcystic lymphangioma · Superficial lymphangioma · Superficial lymphatic malformation
What it is
A rare common cystic lymphatic malformation characterized by a benign cystic lesion composed of dilated lymphatic channels. Microcystic lesions consist of cysts smaller than 1 cm in diameter. They usually present at birth or during the first years of life and most often occur in the head and neck region but may affect any site. Symptoms depend on the location and extent of the lesion. Infection, trauma, or intracystic hemorrhage can lead to lesional expansion. Malignant transformation does not occur.
Key facts
- Age of onset
- Infancy, Neonatal
- Inheritance
- Not applicable
- Classified as
- Clinical subtype
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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