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Start free with EleplanLipomatous non-saccular limited dorsal myeloschisis
ORPHA:645300Histopathological subtype
Also called Lipomatous flat LDM · Lipomatous flat limited dorsal myeloschisis · Lipomatous non-saccular LDM
What it is
A rare non-saccular limited dorsal myeloschisis histologically characterized by skin tissue with a jagged depression of squamous epithelium continued to subcutaneous mature adipose tissue with loose connective tissue. GFAP-immunopositive glial cells are embedded in the subcutaneous lipoma. The extradural and intradural stalk have cord-like fibrocollagenous tissue containing adipose tissue, peripheral nerve fibers, clusters of melanocytes, and skeletal muscle fibers.
Key facts
- Inheritance
- Unknown
- Classified as
- Histopathological subtype
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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