Functioning neuroendocrine tumor of…

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Functioning neuroendocrine tumor of pancreas

ORPHA:506060Category

Also called Functioning PNET · Functioning pancreatic NET · Functioning pancreatic neuroendocrine tumor · Functioning well-differentiated NEN of pancreas · Functioning well-differentiated neuroendocrine neoplasm of pancreas · Functioning well-differentiated pancreatic NEN · Functioning well-differentiated pancreatic neuroendocrine neoplasm

What it is

Orphanet has not published a description for this disease yet. The identifiers, classification and cross-references below are still current.

Key facts

Age of onset
Adult, Elderly
Classified as
Category

Recorded for the broader condition

Prevalence
1-9 / 100 000 (Japan)Neuroendocrine tumor of pancreas
Inheritance
Autosomal dominant, Not applicableNeuroendocrine tumor of pancreas

Orphanet records these for the broader condition rather than for this specific form. They are a starting point, not a figure for this subtype — subtypes often differ, and some are defined by being rarer than the condition they sit under.

Genes reported in subtypes

MEN1YY1

Orphanet records these genes on 1 more specific entry under this disorder, not on this entry itself:

A well-studied disease is usually split into subtypes, and the gene is curated on whichever one the evidence belongs to. Open a subtype to see which gene goes with it.

Cross-references

MONDO 0023206UMLS C1708107

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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