Congenital pericardium anomaly

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Congenital pericardium anomaly

ORPHA:2846Category

What it is

Congenital pericardium anomaly comprises a group of rare congenital cardiac malformations characterized by the complete (Congenital complete agenesis of pericardium) or partial absence of the pericardium (Congenital partial agenesis of pericardium), or by the presence of pericardial cysts (Pleuropericardial cyst).

Key facts

Age of onset
All ages
Inheritance
Not applicable
Classified as
Category

Recorded for the broader condition

Prevalence
>1 / 1000 (at birth, Canada)Rare congenital heart disease

Orphanet records these for the broader condition rather than for this specific form. They are a starting point, not a figure for this subtype — subtypes often differ, and some are defined by being rarer than the condition they sit under.

Cross-references

MONDO 0017300MONDO 17300UMLS C0685699

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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