Autoimmune pancreatitis

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Autoimmune pancreatitis

ORPHA:103919Clinical group

Also called AIP

What it is

A rare pancreatic disease characterized by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type 1, which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2, which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.

Key facts

Inheritance
Not applicable
Classified as
Clinical group

Cross-references

GARD 10911MEDDRA 10069002MESH D000081012MONDO 0015175MONDO 15175UMLS C2609129

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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