Atresia of urethra

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Atresia of urethra

ORPHA:105Morphological anomaly

Also called Urethral atresia

What it is

A rare fetal lower urinary tract obstruction (LUTO) characterized by closure or failure to develop an opening in the urethra and resulting in obstructive uropathy presenting in utero as megacystis, oligohydramnios or anhydramnios, and potter sequence.

Key facts

Age of onset
Antenatal, Neonatal
Inheritance
Not applicable
Classified as
Morphological anomaly

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

ICD-10 codes

Q64.3ICD-10 names this disease exactly

Cross-references

MEDDRA 10064895MONDO 0015195UMLS C0345345

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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