Acquired arginine vasopressin deficiency

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Acquired arginine vasopressin deficiency

ORPHA:95626Clinical subtype

Also called Acquired CDI · Acquired neurogenic diabetes insipidus

What it is

A subtype of central diabetes insipidus (CDI) characterized by polyuria and polydipsia, due to an idiopathic or secondary decrease in vasopressin (AVP) production.

Key facts

Age of onset
All ages
Classified as
Clinical subtype

Recorded for the broader condition

Prevalence
1-9 / 100 000 (Europe)Arginine vasopressin deficiency
Inheritance
Autosomal dominant, Autosomal recessive, X-linked dominantArginine vasopressin deficiency

Orphanet records these for the broader condition rather than for this specific form. They are a starting point, not a figure for this subtype — subtypes often differ, and some are defined by being rarer than the condition they sit under.

Signs and symptoms

Common30–79%

1

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

ICD-10 codes

E23.2filed under a broader ICD-10 category — shared with 2 other rare diseases

ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Benefit programs to look at

Programs whose eligibility touches the same ICD-10 categories. Eligibility is decided by the administering agency, never by this page.

Cross-references

MONDO 0019846UMLS C5680256

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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