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Start free with EleplanRegional odontodysplasia
ORPHA:83450Disease
Also called Ghost teeth
What it is
A rare orodental disease characterized by localized developmental anomaly of the dental tissues, with enamel and dentin hypomineralization affecting one (odontodysplasia) or several (regional odontodysplasia; ROD) teeth (deciduous and permanent, with teeth of the maxilla more frequently involved).
Key facts
- Age of onset
- Childhood
- Inheritance
- Not applicable
- Classified as
- Disease
Signs and symptoms
Common30–79%
17- Abnormality of dental color
- Abnormality of dental enamel
- Abnormality of dentin
- Abnormality of primary teeth
- Abnormality of the dental pulp
- Carious teeth
- Delayed eruption of teeth
- Dental enamel pits
- Enamel hypoplasia
- Gingivitis
- Hypocalcification of dental enamel
- Jaw pain
- Odontodysplasia
- Pulp calcification
- Tooth abscess
- Unerupted tooth
- Yellow-brown discoloration of the teeth
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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