Congenital syphilis

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Congenital syphilis

ORPHA:499009Disease

Also called MTCT of syphilis · Mother-to-child transmission of syphilis

What it is

A rare teratologic disease caused by vertical transmission of the spirochete Treponema pallidum from an infected mother to the fetus, characterized by early congenital syphilis during the first two years of life (maculopapular rash progressing to desquamation, hepatosplenomegaly, osteochondritis, snuffles, and iritis), followed by late congenital syphilis with the classic Hutchinson's triad of Hutchinson's teeth, interstitial keratitis, and eighth nerve deafness. Additional signs may include saddle nose, saber shins, seizures, and mental retardation. Congenital syphilis can also result in stillbirth, neonatal death, and nonimmune hydrops.

Key facts

Prevalence
1-9 / 100 000 (Europe)
Age of onset
Antenatal, Neonatal
Inheritance
Not applicable
Classified as
Disease

Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.

Signs and symptoms

These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.

ICD-10 codes

A50.0ICD-10 uses a narrower term
A50.1ICD-10 uses a narrower term
A50.2ICD-10 uses a narrower term
A50.3ICD-10 uses a narrower term
A50.4ICD-10 uses a narrower term
A50.5ICD-10 uses a narrower term
A50.6ICD-10 uses a narrower term

Related health topics

Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.

Cross-references

MEDDRA 10010641MESH D013590MONDO 0005714UMLS C0039131

Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.

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