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Start free with EleplanMitochondrial non-syndromic sensorineural deafness
ORPHA:90641Etiological subtype
Also called Isolated mitochondrial neurosensory deafness · Isolated mitochondrial neurosensory hearing loss · Isolated mitochondrial sensorineural deafness · Isolated mitochondrial sensorineural hearing loss · Mitochondrial non-syndromic neurosensory deafness · Mitochondrial non-syndromic neurosensory hearing loss · Mitochondrial non-syndromic sensorineural hearing loss
What it is
Orphanet has not published a description for this disease yet. The identifiers, classification and cross-references below are still current.
Key facts
- Age of onset
- Childhood, Infancy
- Inheritance
- Mitochondrial inheritance
- Classified as
- Etiological subtype
Genes
2 modifying genes — variants that can change how the disease behaves, not cause it
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Benefit programs to look at
Programs whose eligibility touches the same ICD-10 categories. Eligibility is decided by the administering agency, never by this page.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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