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Start free with EleplanLegg-Calvé-Perthes disease
ORPHA:2380Disease
Also called Aseptic necrosis of the capital femoral epiphysis · Osteochondrosis of the capital femoral epiphysis · Perthes disease
What it is
A rare osteochondrosis characterized by uni- or bilateral avascular necrosis (AVN) of the femoral head in children.
Key facts
- Prevalence
- 1-9 / 100 000 (annual incidence)
- Age of onset
- Childhood
- Inheritance
- Autosomal dominant, Multigenic/multifactorial
- Classified as
- Disease
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Signs and symptoms
These ranges are how often a sign appears across everyone diagnosed, not a prediction for one person — most people have some of these and not others. Orphanet also records findings that are specifically absent in this disease; those are in the data but not listed here.
Gene
ICD-10 codes
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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