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Start free with EleplanSpontaneous intestinal perforation
ORPHA:645793Disease
Also called FIP · Focal intestinal perforation · Isolated perforation · Neonatal focal intestinal perforation · SIP
What it is
A rare intestinal disease characterized by a single, focal intestinal perforation, associated with hemorrhagic necrosis, typically occurring at the terminal ileum, involving antimesenteric border. It may also occur in the jejunum or colon. It predominantly affects very (or extremely) low weight infants (birth weight less than 1500 g) mostly in the first week of life. Patients have healthy bowel apart from the perforation site, they present with bluish discoloration and gasless abdomen in the absence of pneumatosis intestinalis. Urinary tract infection can also be present. However they do not manifest necrotizing enterocolitis, bowel obstruction or prodromal clinical symptoms.
Key facts
- Inheritance
- Not applicable
- Classified as
- Disease
ICD-10 codes
Related health topics
Reached through the ICD-10 categories this disease is filed under, so these describe the broader group rather than this disease specifically.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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