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Start free with EleplanRenal agenesis, unilateral
ORPHA:93100Clinical subtype
What it is
A form of renal agenesis characterized by the complete absence of development of one kidney accompanied by an absent ureter.
Key facts
- Prevalence
- 1-5 / 10 000 (at birth)
- Age of onset
- All ages, Antenatal
- Inheritance
- Autosomal dominant
- Classified as
- Clinical subtype
Prevalence figures describe populations, not individuals, and are often estimates from a single study. Where the figure is an incidence or a birth prevalence, it says so.
Genes
ICD-10 codes
ICD-10 has no distinct code for most rare diseases, so many are filed under the nearest available one. A shared code identifies the group, not this disease — the ORPHAcode above is what identifies it.
Cross-references
Orphadata Science: Free access data from Orphanet. © INSERM 1999. Data version 2026-06-23. Available under CC BY 4.0. This is a reference, not medical advice.
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